{"id":2112,"date":"2024-07-11T14:38:07","date_gmt":"2024-07-11T13:38:07","guid":{"rendered":"https:\/\/boks.be\/heredite\/"},"modified":"2025-04-16T08:10:21","modified_gmt":"2025-04-16T07:10:21","slug":"heredite","status":"publish","type":"page","link":"https:\/\/boks.be\/fr\/heredite\/","title":{"rendered":"H\u00e9r\u00e9dit\u00e9"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"2112\" class=\"elementor elementor-2112 elementor-686\" data-elementor-post-type=\"page\">\n\t\t\t\t<section class=\"elementor-element elementor-element-328223c e-flex e-con-boxed e-con e-parent\" data-id=\"328223c\" data-element_type=\"container\" data-e-type=\"container\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-08669be elementor-widget__width-auto elementor-widget elementor-widget-heading\" data-id=\"08669be\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Maladies m\u00e9taboliques<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-b8a6372 elementor-widget__width-initial elementor-widget elementor-widget-heading\" data-id=\"b8a6372\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Tout sur l'h\u00e9r\u00e9dit\u00e9<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-f83106e elementor-widget__width-initial elementor-widget elementor-widget-text-editor\" data-id=\"f83106e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les maladies m\u00e9taboliques sont des maladies h\u00e9r\u00e9ditaires. La majorit\u00e9 des maladies m\u00e9taboliques sont autosomiques r\u00e9cessives. <\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/section>\n\t\t<section class=\"elementor-element elementor-element-a629b38 e-flex e-con-boxed e-con e-parent\" data-id=\"a629b38\" data-element_type=\"container\" data-e-type=\"container\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t<div class=\"elementor-element elementor-element-5257ced e-con-full e-flex e-con e-child\" data-id=\"5257ced\" data-element_type=\"container\" data-e-type=\"container\">\n\t\t\t\t<div class=\"elementor-element elementor-element-03c4e7e elementor-widget elementor-widget-heading\" data-id=\"03c4e7e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Autosomique r\u00e9cessif<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-aaea567 elementor-widget elementor-widget-text-editor\" data-id=\"aaea567\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Autosomique r\u00e9cessif signifie que le g\u00e8ne anormal est situ\u00e9 sur l&rsquo;un des 22 chromosomes communs. Les gar\u00e7ons comme les filles peuvent \u00eatre malades. R\u00e9cessif signifie qu&rsquo;il faut deux g\u00e8nes anormaux pour \u00eatre atteint de la maladie. Un enfant atteint d&rsquo;une maladie m\u00e9tabolique a h\u00e9rit\u00e9 d&rsquo;un g\u00e8ne anormal de ses deux parents. Les parents eux-m\u00eames ne sont pas malades et ignorent souvent qu&rsquo;ils sont porteurs. \u00c0 chaque grossesse, ces parents ont 25 % de chances d&rsquo;avoir un enfant atteint d&rsquo;une maladie m\u00e9tabolique, qui n&rsquo;appara\u00eet donc souvent qu&rsquo;\u00e0 la naissance. Ils ont \u00e9galement 50% de chances d&rsquo;avoir un enfant qui n&rsquo;est pas malade, mais qui est porteur. Les enfants ne peuvent transmettre la maladie que si leur partenaire pr\u00e9sente \u00e9galement la m\u00eame anomalie sur son ADN.       <\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-943d817 elementor-widget elementor-widget-image\" data-id=\"943d817\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img fetchpriority=\"high\" decoding=\"async\" width=\"500\" height=\"333\" src=\"https:\/\/boks.be\/wp-content\/uploads\/autosomaal-recessief.png\" class=\"attachment-full size-full wp-image-1755\" alt=\"\" srcset=\"https:\/\/boks.be\/wp-content\/uploads\/autosomaal-recessief.png 500w, https:\/\/boks.be\/wp-content\/uploads\/autosomaal-recessief-300x200.png 300w\" sizes=\"(max-width: 500px) 100vw, 500px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-202d043 e-con-full e-flex e-con e-child\" data-id=\"202d043\" data-element_type=\"container\" data-e-type=\"container\">\n\t\t\t\t<div class=\"elementor-element elementor-element-4e6159f elementor-widget elementor-widget-heading\" data-id=\"4e6159f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Dominant autosomique<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-7f4ff42 elementor-widget elementor-widget-text-editor\" data-id=\"7f4ff42\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Autosomique signifie que le g\u00e8ne anormal est situ\u00e9 sur l&rsquo;un des 22 chromosomes communs. Les gar\u00e7ons comme les filles peuvent \u00eatre malades. En outre, un seul g\u00e8ne (dominant) anormal est d\u00e9j\u00e0 \u00e0 l&rsquo;origine de la maladie. Dans ce cas, le g\u00e8ne normal ne compense pas suffisamment. Chez un enfant atteint d&rsquo;une maladie autosomique dominante, l&rsquo;un des parents est porteur d&rsquo;un g\u00e8ne dominant anormal. Ce parent est \u00e9galement atteint de la maladie. Une personne atteinte d&rsquo;une maladie autosomique dominante a 50 % de chances d&rsquo;avoir un enfant atteint de la m\u00eame maladie.     <\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-5a18056 elementor-widget elementor-widget-image\" data-id=\"5a18056\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"499\" height=\"333\" src=\"https:\/\/boks.be\/wp-content\/uploads\/autosomaal-dominant.png\" class=\"attachment-large size-large wp-image-1758\" alt=\"\" srcset=\"https:\/\/boks.be\/wp-content\/uploads\/autosomaal-dominant.png 499w, https:\/\/boks.be\/wp-content\/uploads\/autosomaal-dominant-300x200.png 300w\" sizes=\"(max-width: 499px) 100vw, 499px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/section>\n\t\t<section class=\"elementor-element elementor-element-9e97863 e-flex e-con-boxed e-con e-parent\" data-id=\"9e97863\" data-element_type=\"container\" data-e-type=\"container\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t<div class=\"elementor-element elementor-element-16b1482 e-con-full e-flex e-con e-child\" data-id=\"16b1482\" data-element_type=\"container\" data-e-type=\"container\">\n\t\t\t\t<div class=\"elementor-element elementor-element-19598b2 elementor-widget elementor-widget-heading\" data-id=\"19598b2\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">R\u00e9cessif li\u00e9 au chromosome X<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-271c3e5 elementor-widget elementor-widget-text-editor\" data-id=\"271c3e5\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les maladies m\u00e9taboliques peuvent \u00e9galement \u00eatre transmises de mani\u00e8re r\u00e9cessive li\u00e9e au sexe. Ce terme signifie que le g\u00e8ne anormal est situ\u00e9 sur un chromosome sexuel, presque toujours sur le chromosome X. Ces maladies surviennent presque exclusivement chez les gar\u00e7ons et les hommes, car ils ne poss\u00e8dent qu&rsquo;un seul chromosome X. Si leur m\u00e8re poss\u00e8de un g\u00e8ne anormal sur l&rsquo;un de ses chromosomes X, elle n&rsquo;est g\u00e9n\u00e9ralement pas malade elle-m\u00eame, car son autre chromosome X contient toujours le g\u00e8ne normal. Ses fils ont une chance sur deux d&rsquo;h\u00e9riter de la maladie. Ses filles sont en bonne sant\u00e9, mais ont une chance sur deux d&rsquo;\u00eatre porteuses du g\u00e8ne anormal. Elles peuvent \u00e9galement transmettre la maladie \u00e0 leurs fils. L\u00e0 encore, on ignore souvent que les femmes sont porteuses jusqu&rsquo;\u00e0 ce qu&rsquo;un fils naisse avec une maladie m\u00e9tabolique.       <\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-93fea13 elementor-widget elementor-widget-image\" data-id=\"93fea13\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"499\" height=\"333\" src=\"https:\/\/boks.be\/wp-content\/uploads\/X-gebonden-recessief.png\" class=\"attachment-full size-full wp-image-1767\" alt=\"\" srcset=\"https:\/\/boks.be\/wp-content\/uploads\/X-gebonden-recessief.png 499w, https:\/\/boks.be\/wp-content\/uploads\/X-gebonden-recessief-300x200.png 300w\" sizes=\"(max-width: 499px) 100vw, 499px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-9d42c71 e-con-full e-flex e-con e-child\" data-id=\"9d42c71\" data-element_type=\"container\" data-e-type=\"container\">\n\t\t\t\t<div class=\"elementor-element elementor-element-6d691b8 elementor-widget elementor-widget-heading\" data-id=\"6d691b8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">N\u00e9omutation<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-22d119a elementor-widget elementor-widget-text-editor\" data-id=\"22d119a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Lorsque les patients contractent la maladie en raison d&rsquo;une nouvelle mutation du g\u00e8ne, la mutation provient du patient lui-m\u00eame et n&rsquo;a donc pas \u00e9t\u00e9 h\u00e9rit\u00e9e de ses parents.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-02999b9 elementor-widget__width-initial elementor-widget elementor-widget-image\" data-id=\"02999b9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img loading=\"lazy\" decoding=\"async\" width=\"1200\" height=\"675\" src=\"https:\/\/boks.be\/wp-content\/uploads\/De-novo-mutatie.png\" class=\"attachment-full size-full wp-image-1761\" alt=\"\" srcset=\"https:\/\/boks.be\/wp-content\/uploads\/De-novo-mutatie.png 1200w, https:\/\/boks.be\/wp-content\/uploads\/De-novo-mutatie-300x169.png 300w, https:\/\/boks.be\/wp-content\/uploads\/De-novo-mutatie-1024x576.png 1024w, https:\/\/boks.be\/wp-content\/uploads\/De-novo-mutatie-768x432.png 768w\" sizes=\"(max-width: 1200px) 100vw, 1200px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Maladies m\u00e9taboliques Tout sur l&rsquo;h\u00e9r\u00e9dit\u00e9 Les maladies m\u00e9taboliques sont des maladies h\u00e9r\u00e9ditaires. La majorit\u00e9 des maladies m\u00e9taboliques sont autosomiques r\u00e9cessives. Autosomique r\u00e9cessif Autosomique r\u00e9cessif signifie que le g\u00e8ne anormal est situ\u00e9 sur l&rsquo;un des 22 chromosomes communs. Les gar\u00e7ons comme les filles peuvent \u00eatre malades. R\u00e9cessif signifie qu&rsquo;il faut deux g\u00e8nes anormaux pour \u00eatre atteint [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"class_list":["post-2112","page","type-page","status-publish","hentry"],"acf":[],"_links":{"self":[{"href":"https:\/\/boks.be\/fr\/wp-json\/wp\/v2\/pages\/2112","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/boks.be\/fr\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/boks.be\/fr\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/boks.be\/fr\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/boks.be\/fr\/wp-json\/wp\/v2\/comments?post=2112"}],"version-history":[{"count":1,"href":"https:\/\/boks.be\/fr\/wp-json\/wp\/v2\/pages\/2112\/revisions"}],"predecessor-version":[{"id":2113,"href":"https:\/\/boks.be\/fr\/wp-json\/wp\/v2\/pages\/2112\/revisions\/2113"}],"wp:attachment":[{"href":"https:\/\/boks.be\/fr\/wp-json\/wp\/v2\/media?parent=2112"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}